CHERUBISM – ORBITAL INVOLVEMENT & TREATMENT
Orbital Involvement in cherubism, Clinical and Experimental Ophthalmology 29: 38-40, 2001, Caroll, Andrew L. and Sullivan, Timothy J.
This case report describes a procedure to debulk orbital and maxillary lesions in a 7 year old with extensive involvement of cherubism in these regions. The surgeons viewed the “potential risk of compressive optic neuropathy” as justification to undertake the intervention.
Orbital Involvement in Cherubism, American Academy of Opthamology 1884-1888, 2001, Colombu, Cursiefen, Neukam, & Holbach.
This article describes surgery conducted to alter cherubism in the orbits. Cherubic lesions in this reason are a cosmetic concern, but can pose a threat to sight. The orbital lesions developed after lesions in the mandible and maxilla regressed spontaneously in this 27 year-old woman. The article reviews the small published literature on cherubism in the orbits. The article provides good photos of the patient and diagnostic images of cherubism, including CT scans and photomicrographs.
Giant Cell Reparative Granuloma of the Orbit Associated with Cherubism,
Ophthalmology 110 (9): 1846-1849, 2003, Font, Ramon L; Blanco, Gonzalo; Soparker, Charles N.; Patrinely, James R.; Ostrowski, Mary L.
This case report involves a 27 year old woman: her cherubism was diagnosed at age 4, it did not regress after puberty and she underwent 3 maxillary and mandibular osteoplasties between ages 18 and 24. Severe visual symptoms did not emerge with the onset of the disease, but later in adulthood. The authors describe the visual distortions associated with the patient’s orbital lesions, the surgical treatments that were undertaken to alleviate the symptoms, and the results.
Optic Neuropathy and Macular Chorioretinal Folds Caused by Orbital Cherubism, Archives of Ophthalmology 121: 570-573, 2003, Ahmadi, A.J.; Pirinjian, Goarik E; Sires, Bryan S.
These authors describe a case of maxillary cherubism that extended into the orbit with “documented visual loss secondary to optic neuropathy and macular chorioretinal folds/ scarring directly attributable to compression from fibro osseous growth within the orbit.” They provide a detailed discussion of the surgical intervention they performed on the 31 year old woman and photographic images of the fundus and cranial CTs taken before and after the surgery.